{"id":2760,"date":"2024-10-10T17:16:32","date_gmt":"2024-10-10T20:16:32","guid":{"rendered":"https:\/\/mbinitiative.org\/?page_id=2760"},"modified":"2025-02-04T11:49:34","modified_gmt":"2025-02-04T14:49:34","slug":"sobre-o-meduloblastoma","status":"publish","type":"page","link":"https:\/\/mbinitiative.org\/pt\/sobre-o-meduloblastoma\/","title":{"rendered":"O que \u00e9 meduloblastoma ?"},"content":{"rendered":"<div data-elementor-type=\"wp-page\" data-elementor-id=\"2760\" class=\"elementor elementor-2760\" data-elementor-post-type=\"page\">\n\t\t\t\t<div class=\"elementor-element elementor-element-ea9f624 e-flex e-con-boxed e-con e-parent\" data-id=\"ea9f624\" data-element_type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-296b965 elementor-widget elementor-widget-heading\" data-id=\"296b965\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h1 class=\"elementor-heading-title elementor-size-default\">Sobre o meduloblastoma<\/h1>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-e7a7dd3 elementor-widget-divider--view-line elementor-widget elementor-widget-divider\" data-id=\"e7a7dd3\" data-element_type=\"widget\" data-widget_type=\"divider.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-divider\">\n\t\t\t<span class=\"elementor-divider-separator\">\n\t\t\t\t\t\t<\/span>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-62dc264 e-flex e-con-boxed e-con e-child\" data-id=\"62dc264\" data-element_type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-e426e35 elementor-widget elementor-widget-heading\" data-id=\"e426e35\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">O que \u00e9 meduloblastoma?<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-5df516a elementor-widget__width-inherit elementor-widget elementor-widget-text-editor\" data-id=\"5df516a\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><img fetchpriority=\"high\" decoding=\"async\" class=\"alignright wp-image-2761\" src=\"https:\/\/mbinitiative.org\/wp-content\/uploads\/2024\/10\/Thank-You-2-300x300.png\" alt=\"\" width=\"288\" height=\"288\" srcset=\"https:\/\/mbinitiative.org\/wp-content\/uploads\/2024\/10\/Thank-You-2-300x300.png 300w, https:\/\/mbinitiative.org\/wp-content\/uploads\/2024\/10\/Thank-You-2-1024x1024.png 1024w, https:\/\/mbinitiative.org\/wp-content\/uploads\/2024\/10\/Thank-You-2-150x150.png 150w, https:\/\/mbinitiative.org\/wp-content\/uploads\/2024\/10\/Thank-You-2-768x768.png 768w, https:\/\/mbinitiative.org\/wp-content\/uploads\/2024\/10\/Thank-You-2-1536x1536.png 1536w, https:\/\/mbinitiative.org\/wp-content\/uploads\/2024\/10\/Thank-You-2-12x12.png 12w, https:\/\/mbinitiative.org\/wp-content\/uploads\/2024\/10\/Thank-You-2.png 1728w\" sizes=\"(max-width: 288px) 100vw, 288px\" \/><\/p><p class=\"translation-block\">O meduloblastoma \u00e9 o tumor cerebral maligno mais comum em crian\u00e7as, correspondendo a quase 20% de todos os tumores cerebrais nessa popula\u00e7\u00e3o. Ele se origina em c\u00e9lulas embrion\u00e1rias (fetais) e normalmente \u00e9 descoberto nos primeiros 5 anos de vida. Ele acomete o sistema nervoso central e se desenvolve no cerebelo. O cerebelo \u00e9 a parte do c\u00e9rebro respons\u00e1vel pela coordena\u00e7\u00e3o dos m\u00fasculos, equil\u00edbrio e movimento. O tumor cresce rapidamente e pode se espalhar para outras partes do c\u00e9rebro, por\u00e9m raramente se espalha para outras partes do corpo.<\/p><p>O meduloblastoma possui uma incid\u00eancia anual geral de aproximadamente 5 casos a cada 1 milh\u00e3o na popula\u00e7\u00e3o pedi\u00e1trica. Cerca de 75% dos casos ocorrem em crian\u00e7as com menos de 10 anos, com o pico de incid\u00eancia entre 1-4 e 5-9 anos de idade. A predile\u00e7\u00e3o do tumor por sexo e a incid\u00eancia espec\u00edfica por idade variam entre os grupos. O meduloblastoma, assim como todos os c\u00e2nceres infantis, \u00e9 considerado uma doen\u00e7a rara, pois afeta uma parcela pequena da popula\u00e7\u00e3o. Isso significa que a obten\u00e7\u00e3o de financiamento para pesquisas \u00e9 muito mais dif\u00edcil do que para doen\u00e7as mais prevalentes.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-d4294ea e-flex e-con-boxed e-con e-child\" data-id=\"d4294ea\" data-element_type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-6239e68 elementor-widget elementor-widget-heading\" data-id=\"6239e68\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Sintomas<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-f2263b2 elementor-widget__width-inherit elementor-widget elementor-widget-text-editor\" data-id=\"f2263b2\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Os sintomas do meduloblastoma geralmente aparecem quando o tumor cresce ou causa aumento da press\u00e3o no c\u00e9rebro e podem persistir mesmo ap\u00f3s o tratamento. Os pacientes podem desenvolver:<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-c04ee41 e-flex e-con-boxed e-con e-child\" data-id=\"c04ee41\" data-element_type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-9ac2896 elementor-widget elementor-widget-text-editor\" data-id=\"9ac2896\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li>dificuldade para andar, manter o equil\u00edbrio e realizar movimentos delicados;<\/li><li>dor de cabe\u00e7a, n\u00e1usea, v\u00f4mito, vis\u00e3o borrada\/duplicada, sonol\u00eancia extrema, confus\u00e3o, convuls\u00f5es e desmaios;<\/li><li>fraqueza ou dorm\u00eancia nos bra\u00e7os e\/ou pernas, altera\u00e7\u00f5es no funcionamento da bexiga e\/ou intestino e dor na coluna;<\/li><li>nos poucos casos em que o tumor se espalha para outras partes do corpo pode haver tosse, dor no peito e falta de ar, aumento dos linfonodos e dor nos ossos.<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-78ca19b elementor-widget__width-inherit elementor-widget elementor-widget-text-editor\" data-id=\"78ca19b\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Dependendo da localiza\u00e7\u00e3o do tumor, os sintomas podem variar.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-0523717 e-flex e-con-boxed e-con e-child\" data-id=\"0523717\" data-element_type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-dbf4a76 elementor-widget elementor-widget-heading\" data-id=\"dbf4a76\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Tipos de meduloblastoma<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-bea670c elementor-widget__width-inherit elementor-widget elementor-widget-text-editor\" data-id=\"bea670c\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Os meduloblastomas s\u00e3o classificados em quatro grupos principais com base em fatores moleculares e gen\u00e9ticos e em quatro subtipos histol\u00f3gicos. Essa classifica\u00e7\u00e3o detalhada \u00e9 usada para determinar o progn\u00f3stico (parecer m\u00e9dico, baseado no diagn\u00f3stico, sobre a prov\u00e1vel evolu\u00e7\u00e3o e desfecho da doen\u00e7a) e orientar o tratamento. Os quatro grupos principais s\u00e3o definidos de acordo com o comportamento do tumor:<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-35dbda0 e-flex e-con-boxed e-con e-child\" data-id=\"35dbda0\" data-element_type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t<div class=\"elementor-element elementor-element-bd5ed53 e-flex e-con-boxed e-con e-child\" data-id=\"bd5ed53\" data-element_type=\"container\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;,&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-9ca07eb elementor-widget elementor-widget-heading\" data-id=\"9ca07eb\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Grupo WNT (wingless)<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-bf7b96f elementor-widget elementor-widget-text-editor\" data-id=\"bf7b96f\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Esse \u00e9 o tipo menos comum de meduloblastoma, correspondendo a apenas 11% de todos os meduloblastomas. Os tumores desse grupo s\u00e3o caracterizados por altera\u00e7\u00f5es na via de sinaliza\u00e7\u00e3o WNT (uma rota bioqu\u00edmica importante que pode afetar o crescimento de tumores). Afetam ambos os sexos igualmente e s\u00e3o comumente diagnosticados em crian\u00e7as com 6 a 10 anos de idade. Esse tipo de meduloblastoma tem o melhor progn\u00f3stico: quase 90% dos pacientes sobrevivem por mais de 5 anos ap\u00f3s o diagn\u00f3stico.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-f6b09fa e-flex e-con-boxed e-con e-child\" data-id=\"f6b09fa\" data-element_type=\"container\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;,&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-333a110 elementor-widget elementor-widget-heading\" data-id=\"333a110\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default translation-block\">Grupo SHH (<i>Sonic Hedgehog<\/i>)<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-1537e55 elementor-widget elementor-widget-text-editor\" data-id=\"1537e55\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Esse tipo de meduloblastoma \u00e9 comum em pacientes mais jovens (com menos de 3 anos de idade) e naquelas com 16 anos ou mais. Esses tumores correspondem a 25% de todos os meduloblastomas. O subgrupo SHH \u00e9 associado a muta\u00e7\u00f5es na via Sonic Hedgehog, que controla o desenvolvimento de c\u00e9lulas embrion\u00e1rias e tamb\u00e9m afeta o crescimento de tumores.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-a3ba5cd e-flex e-con-boxed e-con e-child\" data-id=\"a3ba5cd\" data-element_type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t<div class=\"elementor-element elementor-element-4dfe8bd e-flex e-con-boxed e-con e-child\" data-id=\"4dfe8bd\" data-element_type=\"container\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;,&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-0397a48 elementor-widget elementor-widget-heading\" data-id=\"0397a48\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Grupo 3<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-6144152 elementor-widget elementor-widget-text-editor\" data-id=\"6144152\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Os tumores do Grupo 3 s\u00e3o os mais agressivos, com uma taxa de sobrevida global de 50%, e tendem a se espalhar pelos ventr\u00edculos do c\u00e9rebro e pela medula espinhal. O Grupo 3 corresponde a aproximadamente 25% de todos os meduloblastomas e \u00e9 normalmente diagnosticado em pacientes com 3 a 5 anos de idade.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-5a3c68b e-flex e-con-boxed e-con e-child\" data-id=\"5a3c68b\" data-element_type=\"container\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;,&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-6edff42 elementor-widget elementor-widget-heading\" data-id=\"6edff42\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Grupo 4<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-eb12158 elementor-widget elementor-widget-text-editor\" data-id=\"eb12158\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p class=\"translation-block\">Esse \u00e9 o maior e mais comum grupo dos meduloblastomas, representando 35% de todos os casos. Os tumores do Grupo 4 ocorrem mais em meninos. Tumores desse grupo tem bom progn\u00f3stico, exceto em caso de recidiva. O meduloblastoma infantil do Grupo 4 \u00e9 o foco da pesquisa apoiada pela MBI (<strong>The Medulloblastoma Initiative<\/strong>), que, em 2024, aprovou dois ensaios cl\u00ednicos para testar novos tratamentos.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-9cb3b7e e-flex e-con-boxed e-con e-child\" data-id=\"9cb3b7e\" data-element_type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-ec8a0be elementor-widget elementor-widget-heading\" data-id=\"ec8a0be\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Diagn\u00f3stico<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-1c64ead elementor-widget__width-inherit elementor-widget elementor-widget-text-editor\" data-id=\"1c64ead\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Inicialmente, o processo diagn\u00f3stico envolve o hist\u00f3rico m\u00e9dico do paciente e uma avalia\u00e7\u00e3o dos sinais e sintomas relatados. Os testes e procedimentos geralmente utilizados para o diagn\u00f3stico do meduloblastoma incluem:<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-5a6409a e-flex e-con-boxed e-con e-child\" data-id=\"5a6409a\" data-element_type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-d49d533 elementor-widget elementor-widget-text-editor\" data-id=\"d49d533\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><b>Exame neurol\u00f3gico<\/b>: testa a vis\u00e3o, a audi\u00e7\u00e3o, o equil\u00edbrio, a coordena\u00e7\u00e3o e os reflexos, a fim de identificar qual parte do c\u00e9rebro pode estar sendo afetada pelo tumor.<\/li><li><b>Exames de imagem<\/b>: capturam imagens do c\u00e9rebro para determinar o tamanho e a localiza\u00e7\u00e3o do tumor. Esses exames tamb\u00e9m podem revelar a presen\u00e7a de press\u00e3o ou bloqueios no l\u00edquido cefalorraquidiano. A tomografia computadorizada e resson\u00e2ncia magn\u00e9tica s\u00e3o os exames mais comuns.<\/li><li><b>Amostra tecidual<\/b>: embora bi\u00f3psias sejam incomuns em casos de meduloblastoma, podem ser feitas em certas situa\u00e7\u00f5es. Envolvem a utiliza\u00e7\u00e3o de uma agulha para retirar uma amostra do tumor, que \u00e9, ent\u00e3o, analisada em laborat\u00f3rio para determinar se \u00e9 um meduloblastoma.<\/li><li><b>Pun\u00e7\u00e3o lombar<\/b>: envolve a inser\u00e7\u00e3o de uma agulha entre dois ossos da coluna inferior para retirar o l\u00edquido que envolve a medula espinhal (cefalorraquidiano). Esse l\u00edquido \u00e9 testado em laborat\u00f3rio para verificar a presen\u00e7a de c\u00e9lulas tumorais. A pun\u00e7\u00e3o lombar deve ser realizada somente ap\u00f3s controle da press\u00e3o intracraniana e remo\u00e7\u00e3o do tumor.<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-208f88c e-flex e-con-boxed e-con e-child\" data-id=\"208f88c\" data-element_type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-069b0e5 elementor-widget elementor-widget-heading\" data-id=\"069b0e5\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Progn\u00f3stico (chance de recupera\u00e7\u00e3o)<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-4e04c2d elementor-widget__width-inherit elementor-widget elementor-widget-text-editor\" data-id=\"4e04c2d\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>O progn\u00f3stico, ou seja, a chance de recupera\u00e7\u00e3o de uma pessoa com meduloblastoma, depende de v\u00e1rios fatores, como o tipo molecular do tumor, o est\u00e1gio, a quantidade de tumor removida, a idade, o estado de sa\u00fade do paciente no momento do diagn\u00f3stico e a resposta ao tratamento. Nos primeiros anos ap\u00f3s o diagn\u00f3stico, a taxa de mortalidade \u00e9 pr\u00f3xima de 15%. Com os tratamentos atuais, a taxa de cura pode chegar at\u00e9 70-80% em crian\u00e7as e 50-60% em adultos. A taxa de sobreviv\u00eancia em 5 anos para meduloblastoma \u00e9 de aproximadamente 80,6%, mas pode variar.<\/p><p>O tipo espec\u00edfico de meduloblastoma tamb\u00e9m afeta o progn\u00f3stico. Os tumores ativados pela via WNT t\u00eam um progn\u00f3stico melhor do que aqueles ativados pela via SHH ou do Grupo 3 e 4. Em casos de recorr\u00eancia, a taxa de sobreviv\u00eancia em 5 anos cai para menos de 40%.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-c318d59 e-flex e-con-boxed e-con e-child\" data-id=\"c318d59\" data-element_type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-5e5abbf elementor-widget elementor-widget-heading\" data-id=\"5e5abbf\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Tratamento<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-997ff20 elementor-widget__width-inherit elementor-widget elementor-widget-text-editor\" data-id=\"997ff20\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<div class=\"elementor-element elementor-element-997ff20 elementor-widget__width-inherit elementor-widget elementor-widget-text-editor\" data-id=\"997ff20\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\"><div class=\"elementor-widget-container\"><p class=\"translation-block\">Os protocolos atuais de tratamento para o meduloblastoma, introduzidos em grande parte na d\u00e9cada de 1980 e que, em sua maioria, permaneceram inalterados, dependem fortemente de m\u00e9todos citot\u00f3xicos e n\u00e3o direcionados \u2013 como a radioterapia convencional com raio X, que aplica radia\u00e7\u00e3o a todo o tecido em volta do tumor. Apesar dos avan\u00e7os, as taxas de mortalidade para meduloblastoma continuam elevadas, e muitos sobreviventes sofrem efeitos colaterais de longo prazo devido \u00e0 radioterapia e quimioterapia citot\u00f3xica, assim como dificuldades cognitivas, problemas psicol\u00f3gicos e sociais e at\u00e9 defici\u00eancias hormonais. Esses efeitos podem exigir apoio cont\u00ednuo para melhorar a qualidade de vida dos pacientes, principalmente crian\u00e7as, que s\u00e3o muito mais sens\u00edveis aos efeitos da radioterapia, visto que seus corpos ainda est\u00e3o crescendo e em desenvolvimento.<\/p><p>O tratamento do meduloblastoma geralmente combina cirurgia, radioterapia e quimioterapia. O tratamento inicial envolve a remo\u00e7\u00e3o cir\u00fargica do tumor, seguida de radioterapia e quimioterapia, dependendo do tipo e localiza\u00e7\u00e3o do tumor e do quanto ele se espalhou. Terapia com feixe de pr\u00f3tons (um tipo de radioterapia mais precisa do que o tratamento com raio X convencional, direcionada especificamente ao tumor) pode ser recomendada para reduzir os danos a outros \u00f3rg\u00e3os. Os tratamentos dispon\u00edveis atualmente est\u00e3o descritos em detalhe abaixo.<\/p><\/div><\/div><div class=\"elementor-element elementor-element-c9a24d5 e-flex e-con-boxed e-con e-child\" data-id=\"c9a24d5\" data-element_type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\"><div class=\"e-con-inner\"><div class=\"elementor-element elementor-element-1129e03 elementor-widget elementor-widget-text-editor\" data-id=\"1129e03\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\"><div class=\"elementor-widget-container\"><ul><li><strong>Cirurgia para aliviar a press\u00e3o intracraniana<\/strong>: o meduloblastoma pode crescer e bloquear o fluxo do l\u00edquido cefalorraquidiano, causando um ac\u00famulo que pressiona o c\u00e9rebro. Para reduzir essa press\u00e3o, um cirurgi\u00e3o cria um caminho para que o l\u00edquido flua para fora do c\u00e9rebro. Esse procedimento pode ser combinado com a cirurgia de remo\u00e7\u00e3o do tumor.<\/li><li class=\"translation-block\"><strong>Cirurgia para remover o tumor:  <\/strong>o objetivo da cirurgia \u00e9 remover\u00a0<u>todo<\/u>\u00a0o tumor. No entanto, se ele estiver localizado perto de estruturas importantes do c\u00e9rebro, isso pode n\u00e3o ser poss\u00edvel. A maioria das pessoas com meduloblastoma precisar\u00e1 de tratamentos adicionais ap\u00f3s a cirurgia para eliminar c\u00e9lulas cancerosas restantes.<\/li><li><strong>Radioterapia<\/strong>: A radioterapia utiliza feixes de energia poderosos para matar c\u00e9lulas cancerosas. Essa energia pode vir de raios X, pr\u00f3tons ou outras fontes. Durante a radioterapia, uma m\u00e1quina direciona os feixes de energia para pontos espec\u00edficos do corpo. Costuma ser realizada ap\u00f3s a cirurgia.<\/li><li><strong>Quimioterapia<\/strong>: a quimioterapia usa medicamentos para matar c\u00e9lulas cancerosas. Geralmente, crian\u00e7as e adultos com meduloblastoma recebem esses medicamentos por meio de inje\u00e7\u00f5es intravenosas. A quimioterapia pode ser administrada ap\u00f3s a ressec\u00e7\u00e3o cir\u00fargica ou radioterapia e, em alguns casos, pode ser feita ao mesmo tempo que a radioterapia.<\/li><\/ul><\/div><\/div><\/div><\/div>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-c9a24d5 e-flex e-con-boxed e-con e-child\" data-id=\"c9a24d5\" data-element_type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-48abaed e-flex e-con-boxed e-con e-child\" data-id=\"48abaed\" data-element_type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-932f0fc elementor-widget elementor-widget-heading\" data-id=\"932f0fc\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Perspectivas futuras<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-c1cf043 elementor-widget__width-inherit elementor-widget elementor-widget-text-editor\" data-id=\"c1cf043\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Ensaios cl\u00ednicos com novos medicamentos tamb\u00e9m podem ser uma op\u00e7\u00e3o para alguns pacientes. Os ensaios cl\u00ednicos recrutam participantes eleg\u00edveis para estudar novos tratamentos, como imunoterapia, ou novas formas de usar tratamentos existentes, como diferentes combina\u00e7\u00f5es ou dura\u00e7\u00e3o de radioterapia e quimioterapia. Esses estudos oferecem aos pacientes a oportunidade de experimentar op\u00e7\u00f5es de tratamento mais recentes, embora os riscos de efeitos colaterais n\u00e3o sejam totalmente conhecidos.<\/p><p>Desde a sua cria\u00e7\u00e3o em 2021, a MBI vem juntando recursos para achar uma cura para os meduloblastomas do Grupo 4. A MBI conseguiu reunir apoio financeiro para um cons\u00f3rcio de 14 laborat\u00f3rios nos Estados Unidos, Alemanha e Canad\u00e1 (o Cure Group 4 Consortium), liderado pelo Dr. Roger Packer do Children\u2019s National Hospital. O grupo j\u00e1 fez uma descoberta significativa sobre o prov\u00e1vel mecanismo de desenvolvimento das c\u00e9lulas que d\u00e3o origem ao meduloblastoma.<\/p><p>Al\u00e9m disso, em menos de 3 anos, dois ensaios cl\u00ednicos j\u00e1 foram aprovados pela Food and Drug Administration (FDA) dos EUA para testar dois novos tratamentos:<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-bc6fb5d e-con-full e-flex e-con e-child\" data-id=\"bc6fb5d\" data-element_type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t<div class=\"elementor-element elementor-element-a9508ec e-flex e-con-boxed e-con e-child\" data-id=\"a9508ec\" data-element_type=\"container\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;,&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-44ed8f8 elementor-widget elementor-widget-text-editor\" data-id=\"44ed8f8\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Estudo 1<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-c56b49b elementor-widget elementor-widget-text-editor\" data-id=\"c56b49b\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Tamb\u00e9m chamado de MATCHPOINT \u2013 ataca os tumores de duas maneiras: 1) treina as pr\u00f3prias c\u00e9lulas do paciente para identificar e destruir as c\u00e9lulas cancer\u00edgenas e 2) usa um medicamento adicional para eliminar o sistema de defesa do tumor.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-23e2776 e-flex e-con-boxed e-con e-child\" data-id=\"23e2776\" data-element_type=\"container\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;,&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t\t<div class=\"e-con-inner\">\n\t\t\t\t<div class=\"elementor-element elementor-element-e40aa89 elementor-widget elementor-widget-text-editor\" data-id=\"e40aa89\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Estudo 2<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-0766e38 elementor-widget elementor-widget-text-editor\" data-id=\"0766e38\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Est\u00e1 testando uma vacina de mRNA \u2013 semelhante \u00e0 vacina contra a COVID-19, mas mais personalizada, j\u00e1 que utiliza as c\u00e9lulas do pr\u00f3prio paciente. A nanotecnologia \u00e9 usada para criar a vacina. Uma vez injetada, a vacina gera uma resposta imune direcionada para destruir os tumores.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-f9faa95 elementor-widget__width-inherit elementor-widget elementor-widget-text-editor\" data-id=\"f9faa95\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Mais tr\u00eas ensaios cl\u00ednicos ser\u00e3o protocolados entre 2024 e 2025. Espera-se que esse esfor\u00e7o apoiado com recursos filantr\u00f3picos encontre a cura para os meduloblastomas do Grupo 4.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t<div class=\"elementor-element elementor-element-b90012a e-con-full e-flex e-con e-child\" data-id=\"b90012a\" data-element_type=\"container\" data-settings=\"{&quot;jet_parallax_layout_list&quot;:[]}\">\n\t\t\t\t<div class=\"elementor-element elementor-element-cb75c9a elementor-widget elementor-widget-heading\" data-id=\"cb75c9a\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Refer\u00eancias<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-64c5ef4 elementor-widget-divider--view-line elementor-widget elementor-widget-divider\" data-id=\"64c5ef4\" data-element_type=\"widget\" data-widget_type=\"divider.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-divider\">\n\t\t\t<span class=\"elementor-divider-separator\">\n\t\t\t\t\t\t<\/span>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-424b366 elementor-widget__width-inherit elementor-widget elementor-widget-text-editor\" data-id=\"424b366\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><a href=\"https:\/\/www.mayoclinic.org\/diseases-conditions\/medulloblastoma\/cdc-20363524\/\">https:\/\/www.mayoclinic.org\/diseases-conditions\/medulloblastoma\/cdc-20363524\/<\/a><\/p><p><a href=\"https:\/\/mbinitiative.org\/pt\/clinical-trails-approved\/\">https:\/\/mbinitiative.org\/pt\/clinical-trails-approved\/<\/a><\/p><p><a href=\"https:\/\/www.ncbi.nlm.nih.gov\/books\/NBK431069\/\">https:\/\/www.ncbi.nlm.nih.gov\/books\/NBK431069\/<\/a><\/p><p><a href=\"https:\/\/braintumourresearch.org\/pages\/types-of-brain-tumours-medulloblastoma?srsltid=AfmBOopoKjcDUKW1NU8mxx6M6ar4i5rNqf3aurkf7H724orjokIhuRf9\">https:\/\/braintumourresearch.org\/pages\/types-of-brain-tumours-medulloblastoma?srsltid=AfmBOopoKjcDUKW1NU8mxx6M6ar4i5rNqf3aurkf7H724orjokIhuRf9<\/a><\/p><p><a href=\"https:\/\/www.cancer.gov\/rare-brain-spine-tumor\/tumors\/medulloblastoma\">https:\/\/www.cancer.gov\/rare-brain-spine-tumor\/tumors\/medulloblastoma<\/a><\/p><p><a href=\"https:\/\/ascopubs.org\/doi\/10.1200\/JCO.2017.72.7842\">https:\/\/ascopubs.org\/doi\/10.1200\/JCO.2017.72.7842<\/a><\/p><p><a href=\"https:\/\/medulloblastoma.org\/medulloblastoma-statistics\/\">https:\/\/medulloblastoma.org\/medulloblastoma-statistics\/<\/a><\/p><p><a href=\"https:\/\/www.sciencedirect.com\/science\/article\/pii\/S1878747923014630\">https:\/\/www.sciencedirect.com\/science\/article\/pii\/S1878747923014630<\/a><\/p><p><a href=\"https:\/\/www.infopedia.pt\/dicionarios\/lingua-portuguesa\/prognstico\">https:\/\/www.infopedia.pt\/dicionarios\/lingua-portuguesa\/prognstico<\/a><\/p><p><a href=\"https:\/\/www.mayoclinic.org\/departments-centers\/proton-beam-therapy-program\/sections\/overview\/ovc-20185491?mc_id=us&amp;utm_source=newsnetwork&amp;utm_medium=l&amp;utm_content=content&amp;utm_campaign=mayoclinic&amp;geo=national&amp;placementsite=enterprise&amp;invsrc=other&amp;cauid=100721\">https:\/\/www.mayoclinic.org\/departments-centers\/proton-beam-therapy-program\/sections\/overview\/ovc-20185491\u2026<\/a><\/p><p><a href=\"https:\/\/mbinitiative.org\/wp-content\/uploads\/2024\/09\/MBI-Report-September-2024-EN.pdf\">https:\/\/mbinitiative.org\/wp-content\/uploads\/2024\/09\/MBI-Report-September-2024-EN.pdf<\/a><\/p><p><a href=\"https:\/\/mbinitiative.org\/wp-content\/uploads\/2024\/04\/Report-MBI-Abril-2024-PT.pdf\">https:\/\/mbinitiative.org\/wp-content\/uploads\/2024\/04\/Report-MBI-Abril-2024-PT.pdf<\/a><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>","protected":false},"excerpt":{"rendered":"<p>Discover a father&#8217;s moving journey to find a cure for childhood cancer and learn how you can support this cause with The Medulloblastoma Initiative.<\/p>","protected":false},"author":4,"featured_media":3103,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"footnotes":""},"class_list":["post-2760","page","type-page","status-publish","has-post-thumbnail","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v26.0 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>The Cure for Childhood Cancer | The Medulloblastoma Initiative<\/title>\n<meta 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